What Is Aggressive Fibromatosis?

The incidence of myofibroma is 1.37% of benign soft tissue tumors. Tumors can occur in large muscles in any part of the body. The rectus abdominis and the aponeurosis of adjacent muscles are the most common. They occur in pregnancy and late pregnancy. Those outside the abdominal wall are more common in men, and are more common in the scapula, thigh and hips. The age of onset is mostly 30 to 50 years old, and children and adolescents are not uncommon. The cause of this disease is unknown, and may be related to trauma, hormones and genetic factors.

Myofibroma

Myofibromas are fibrous tissue tumors derived from muscle, aponeurosis, and fascia and rich in collagen. It is a benign tumor composed of fibrous connective tissue. It is more common to grow slowly under the skin and generally always have smaller edges. Since the surface is smooth and the texture is hard, it can be promoted to become fibroids, fibroadenomas, fibrolipomas, etc. if mixed with other ingredients.

Incidence of myofibroma

Myofibroma pathology

The tumor was found to be rich in collagen fibers under the microscope. The lesion had no envelope and had no boundary with the surrounding tissues. Sometimes the surrounding tissue was included in the lesions. Nuclear fission was rare, and capillaries and fat cells were rare. Morphological changes of fibrosarcoma can occur in a few cases of recurrence.

The tumor is located in deep tissues without noticeable symptoms or slight discomfort. Slow growth. Irregular shape or oval shape, its long diameter is consistent with the direction of affected muscle fibers. The size of the tumor is related to the length of the disease, ranging from a few centimeters to a dozen centimeters in diameter. The perimeter of the tumor is unclear, the surface is smooth, there is no tenderness, and the quality is tough like rubber. It is relatively fixed in the longitudinal direction with muscle invasion, but slightly movable in the horizontal direction, without adhesion to the skin. Giant tumors can affect activity and compress nerves.

Myofibroma type

1. Yellow muscle fibroids: Occurs in the dermis or subcutaneous layer of the upper arm near the trunk. The small papular masses often start from trauma or pruritus. The hard edges are unclear. cm grows fast, it should be suspected that children with fibrosarcoma surgery must be completely removed

2. Carina cutaneous fibrosarcoma: located on the surface of the dermal layer, the surface of the skin is smooth and scar-like. It occurs in low-grade malignant trunks with pseudo-enveloping personality. It is easy to relapse many times. Early removal of clinical tumors with sufficient normal loved ones' skin and deep adjacent fascia

3. Banded myofibromas: abdominal wall muscles due to trauma or postpartum prosthetic prosthetic hyperplasia, the apparent envelope of the heart should be surgically removed on Monday.

Myofibromatosis symptoms

Lumps grow slowly and generally transfer without much money. Other symptoms are too poor. They are often found under the skin, have no adhesion to the skin, and have a certain degree of activity. Slow growth, usually small, normal skin smooth heart can feel the smooth rounded mass under the skin. The state of no tenderness has clearly seen the texture is hard. A few have malignant biological behaviors, relapse stubbornly many times, but rarely distant metastases. The recurrence rate was 25 to 57%. The recurrence time is mostly from 1 month to 1 year after operation, even up to more than 10 years, so this type of tumor is also called invasive fibromatosis. Repeated recurrences can lead to a wider range of lesions, with irrepressible growth, invasion of vital organs, and life-threatening.

Myofibroma diagnosis

1. It can be found in all parts of the body, ranging from large to small, with a smooth surface or a head shape, which can be viewed freely.

2. It can also be seen that those with pedicles can increase to a few kilograms, more slack hanging, soft to the touch, and pigmentation.

3. According to its tissue composition and nature, there are two special types of soft and hard. Soft fibroids, also known as skin tags, are more common on the face, neck and chest and back, with pedicles, varying in size, and soft and elastic. It is more common in women between 20 and 40 years of age and is more common in the abdominal wall. It is a hard, painless, non-mobile, mass with unclear boundaries with surrounding tissues, which grows slowly, without capsular and infiltrating. It is easy to develop in summer. And hateful change.

4.The pathological section can determine the nature of the tumor.

Myofibroma Treatment

Muscle fibroids should be surgically removed early and appropriate surrounding tissues removed to prevent recurrence. The resection must have a certain breadth and depth. It should include the normal skin, muscles, tendons and other normal tissues of 3 to 5 cm around the tumor. If the tumor invades the periosteum or peritoneum, it should be removed at the same time. If the tumor surrounds important blood vessels and nerves, it should be sharply separated, and if necessary, it can be used for blood vessel transplantation. Grasp the indications of amputation and hemipelvic amputation. Hard fibroids should be treated with early extensive resection radiotherapy and the use of hormones in individual cases to inhibit tumor growth. However, it is generally considered not to be the main treatment and can be used as palliative treatment for those who cannot be operated on.

Extensive tumor resection often results in local soft tissue defects and exposed important tissues. Tissue transplantation must be used to repair the local area. Only by mastering the treatment of tissue transplantation can we create conditions for radical surgery. Local muscle flap or muscle flap repair is ideal. Its advantages are: rich blood flow, easy to survive. Easy to operate. Immediately repair the defect once. Strong anti-infective power. Rich tissue, can be a good pad, can play a buffer role. The rotation arc is large to facilitate the transfer in all directions. If an island muscle flap is formed, it can reach 180 ° inversion.