How can I handle epidermolytic hyperkeratosis?

Epidermolytic hyperkeratosis, also known as a bull -innate ichthyosiform erythroderma, is a rare genetic disorder that causes the skin to become very sensitive and fragile. There is no known remedy for this disorder, but there are several treatment procedures that can help control symptoms. If you have epidermolytic hyperkeratosis, you can handle it by maintaining your skin hydrated skin, frequent long baths and possibly using a topic or oral medication. Finally, the condition leads to reinforcement of the skin. The severity of this condition is very variable.

Skin maintaining properly moistened is perhaps the most important step in managing symptoms if you are influenced by epidermolytic hyperkeratosis. Local plasticizers should be used regularly to prevent scaling. After the skin begins to the scale, you are exposed to an increased risk of skin infection. It seems that the addition of sea salt to the water in the bath has another softening effect. Also facilitates removal of excess skin relatedeating amplification caused by disorder.

If the skin becomes irritated or the associated blisters ignite, your doctor often prescribes local and oral medicines. Antibiotics are used to control any infection that could be present. Anti -inflammatory drugs are used to control any swelling or inflammation of the affected skin.

oral retinoids such as isotretinoin are also used to control symptoms of epidermolytic hyperkeratosis. Isotretinoin is derived from vitamin A and many consider it a miracle cure. This medicine, more often known as Accutane®, is used in the treatment of mild to severe acne. Doctors found limited success in using this treatment and other skin conditions.

gene therapy has been examined as a possibility for those suffering from epidermolytic hyperkeratosis. We hope that gene therapy will eventually be able to do this skin disorder completely eradicked. Meanwhile, proper skin care is still the best defense against some of the most serious symptoms of epidermolytic hyperkeratosis.

Newborns affected by epidermolytic hyperkeratosis are often shifted to a unit of intensive care for newborns to monitor symptoms and provide treatment as needed. In newborns, this condition causes the skin to look as if it has been burned. This new skin is very fragile and can tear quite easily. Fine handling is required as the infection can easily adjust. This may require antibiotic therapy even for the smallest patients.