What is Dentinogenesis Imperfecta?
Dentinogenesis Imperfecta is a genetic disorder that causes teeth to be particularly fragile and faded. The name concerns the poor or abnormal development of the inner material found in the teeth, called dentin. Dentinogenesis of Imperfecta tends to influence both the child and permanent teeth and many patients who gain the condition also suffer from fragility and deformation in their bones. Currently, there is no cure for disorder, but cosmetic dentures are available to improve the appearance and function of the teeth. Scientists have identified several very specific genes that contribute to the growth of hard tissues in the body, including dentin and enamel that make up teeth. When a particular gene is mutated or inactivated, it is unable to produce the proteins needed to create a strong hard dentin. Most cases of dentinogenesis of Imperfecta are inherited in an autosomal dominant pattern that refers to the fact that only one of the parents of the child must bear the gene mutucopia to be handed over.
Most Dentin casesOgenesis Imperfecta is recognizable in early childhood as soon as the primary teeth begin to grow. They are usually smaller than average baby teeth and have a jagged appearance. The teeth often have a gray, brown or yellow shade and may seem partially translucent, because the outer enamel layer is very thin. Children with dentinogenesis of Imperfecta tend to lose their teeth at an earlier age than their peers.
When permanent teeth grow, they share the same unusual properties. Adolescents and adults with condition are prone to easily break the teeth. Poorly aligned teeth usually cannot be repaired by traditional techniques such as braces because they are too fragile. Permanent teeth may begin to fall out in the third or fourth decade of life.
A dentist or pediatrician can do dentinogenesis Imperfecta based on the physical appearance of the teeth. To confirm the presence of mutated genes can be made geneticBlood tests. Dentinogenesis Imperfecta may sometimes be a symptom of a greater basic disorder called osteogenesis of imperfect, which worsens the body's ability to build and maintain strong bones. X -rays with a full body are often used to confirm or exclude bone involvement in patients who are originally observed for teeth problems.
The treatment of dentinogenesis of Imperfectt depends on the severity of the patient's condition and age. In many cases, doctors prefer to wait for permanent teeth to grow over treatment. Options include coverage of damaged teeth in synthetic enamel or assembly on particularly fine or broken teeth that protect them. In some cases, the teeth are completely removed and replaced by permanent artificial implants.