What is a desmoplastic small round cell tumor?

Desmoplastic tumor with small round cells, sometimes called mesothelioblastoma, is a type of sarcoma of soft tissues, which is usually observed in young men. This type of cancer is extremely aggressive and is difficult to heal and the five -year survival rate is bad. This type of cancer usually comes from tissues inside the abdomen, but at a time when the cancer is discovered, it often metastasized into lungs, bones, lymph nodes or brain. Doctors are not sure what causes this type of cancer, although a rare genetic marker can help in a positive diagnosis. Of patients who develop this cancer, 90 percent are men and 85 percent are Caucasian. This disease can affect any person at any age, but in a person over 30 years of age is rarely observed. In most cases, the abdomen is a desmoplastic small round cell tumor. However, these tumors may emerge in any part of the body, including kidney, reproductive organs, skin and pancreas. They can be evenly or irregularLno shaped, although largely appearing as light -colored spherical balls and can be found individually, in clusters or rows. Before these tumors are found, they are often relatively large and can have a diameter of 3.9 inches (10 centimeters) or more.

symptoms of this type of cancer may not be recorded until the desmoplastic small round cell tumor does not create large enough to disrupt bodily functions or the cancer spreads to other parts of the body. Tumors themselves can cause pain and discomfort or gastrointestinal problems. Occasionally they can spread through the abdominal lining and create a swollen space on the skin surface. When this cancer is discovered, it has often spread to other systems, some of which were distant from the original Sinador.

treatment in patients who have a desmoplastic tumor for small round cells is difficult and often not effective. Tumors are often large and many of them canT widespread on the abdomen, making their surgically removal more difficult. They also have the properties of a number of different types of cancer cells, which are resistant to treatment including radiation and chemotherapy. Only about 15 percent of patients diagnosed with this form of cancer will live for 5 or more years.