What is the Erdheim-Chester disease?

Erdheim-cester The disease is a rare medical disorder that causes an abnormally high production of a specific type of white blood cells known as histiocyte. This disease can affect anyone at any age, although it is the most common in men for more than 50 years. Some symptoms of the disease may include bone pain involving arms and legs, weight loss and coordination problems. More serious symptoms often include heart damage, kidney failure and development of abnormal masses or growth throughout the body. Treatment options include the use of prescription drugs, chemotherapy or radiation therapy, although the disease is usually fatal, even in aggressive treatment.

bone pain is the most common symptom of Erdheim-Cester's disease and often includes long bones of arms and legs. This pain is often described as relatively mild, yet constant. Joint and muscle pain are also common among those with this disease, usually cause different weakness and fatigue.

fever, weight lossAnd night sweats are often present in Erdheim-Cester's disease, sometimes leading to an incorrect diagnosis for many years, as these symptoms carry several other conditions. Many more serious symptoms must develop many times before these diseases are diagnosed. Later during the disease, balance and coordination problems develop and the patient may have difficulty breathing or pain.

Since Erdheim-Cester's disease begins to proceed, vital organs such as heart or kidneys may be damaged. Abnormal tissue can begin to grow in or around the heart, leading to a reduction in heart function. The kidneys are also usually affected and dialysis may be necessary to prolong the patient's life. Lung diseases are common and unusual masses or lesions can begin to grow in different areas, including the brain.

Treatment of Erdheim-Cester's disease primarily lies inTreatment of individual symptoms and maintaining the most comfortable patient. This often involves the use of prescription drugs, although some lesions may be treated with radiation or chemotherapy. Surgery may be needed to treat some symptoms or complications related to this disease. Since this disease is affected by several body systems, the condition is usually fatal, even when using aggressive treatment methods. Any individualized questions or concerns about Erdheim-Cester's disease should be discussed with a doctor or other doctor.

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