What is haemophilia?
Hemophilia is a hereditary blood disease that results in the inability of blood normally. Those suffering from this condition can bleed for a long time even from the smallest section or injury. Unexplained bruises are also common. Although bleeding from external injuries is a problem for those suffering from this disease and may be serious, the danger of haemophilia is a tendency to bleed internally. Muscle and joint bleeding is a common pain symptom, but the main internal organs such as the brain, spinal cord, liver and other critical systems can begin to bleed unexpectedly, causing immediate risk. Health workers recognize two different types of haemophilia: type A and type B. These two types differ in the type of protein that is inadequate or absent in the blood. The protein that causes type A is called factor VIII protein and haemophilia B is caused by a protein known as the IX factor.
both types are extremerare; Type A, however, is slightly more common than type B. Hemophilia occurs almost exclusively in men, although female carriers may cause mild symptoms. Individual cases are considered mild, medium or severe depending on the deficiency of proteins that normally help blood clot. Those with mild haemophilia generally have only 30% of the average level of protein clotting. A mild disease is only 5% of normal protein levels and serious results from less than 1% of the normal presence of protein.
Hemophilia is usually diagnosed during the first year of life and modern treatment is effective. Factor substitution therapy using synthetic proteins is the most common and effective treatment. For BOOS, the next summer is available to the production of body proteins or to help clotting by other means.
In history, one of the most famous and tragic cases influenced the intended heir to the throne of Russia. The son of Nicholas II, the last Russian Tsar, Alexei suffered from severe haemophilia. IgnoranceAt that time, T illness caused Alexei's upset parents to trust the mystical rasputin that was able to bring help from his illness. The strength and authority that Rasputin gained through his healing abilities eventually led to the fall of the empire and the demise of Romanov's family. Alexei's disorder inspired a common description of this condition as a "royal disease".