What is Potter's syndrome?

The term potter syndrome concerns the collection of congenital abnormalities present in some newborns. The characteristics of this disease include poor lung development, kidney failure and physical abnormalities. This constellation of abnormalities occurs as a result of kidney disease: low urine output leads to a reduced amniotic fetal fluid, which in turn leads to congenital problems. Although many developing children are diagnosed with this disease, while they are still in the womb, others are diagnosed on the basis of their symptoms at birth. Treatment of this disease is considered a nature and there is no real drug for this disease.

To understand the manifestations of Potter's syndrome, it helps to understand the causes of the state. The initial event leading to syndrome is usually kidney development problems. One cause is the complete absence of the kidneys, also known as bilateral kidney agenesis. Further renal malformations such as polycystic kidney disaobstructionWe can also lead to syndrome as renal hypoplasia. The kidneys usually form urine that contributes to the fetal fluid, the liquid surrounding the developing fetus. Without normal kidney function, reduced fetal fluid occurs, which is a condition referred to as oligohydramnios.

Fruits affected by oligohydramnios secondary to renal dysfunction can develop a number of complications. The amniotic area is usually swallowed by the fetus and without sufficient liquid for ingestion, abdominal and thoracic areas may not grow properly. Developing children also breathe in the amniotic fruit and insufficient amount of fluid can lead to poor lungs. Amniotic fluid also serves as a pillow for the fetus and without this buffer the fetus can develop physical abnormalities.

Potter syndrome can in some cases be diagnosed in the uterus. Routine ultrasonic tests measure the amount of amniotopic fluid and fetus present, which is found to have oligohydramnios, will be exposed to more extensive processing, which could identify kidney insufficiency. Although many cannot be done when the child is still in the womb, pediatricians may be prepared to take care of the child as soon as they are born.

Sometimes potter syndrome is not diagnosed until the child is born. These infants often have respiratory problems due to poor lung development, also known as pulmonary hypoplasia. They have low urine output due to problems with their kidneys. Newborns also have a characteristic face appearance, known as Potter Facies, which develops due to the low volume of amniot fluid and leads to a flattened face of the face wide -set and depressed nasal bridge. Limb abnormalities are also possible due to oligohydramnios in the uterus.

Treatment of Potter's syndrome should first offer supportive care. Disabled children often need respiratory support, either in the form of mechanical ventilation or additional oxygenu. Many of these infants will need dialysis in order to deal with kidney failure. Unfortunately, some of these children have too many congenital abnormalities that need to be adequately treated, and the decision to withdraw care is made by a family.