What is Binder's syndrome?

also referred to as Maxilla-Snacal dysplasia, Binder's syndrome is a rare congenital disease affecting the face and cervical spine. It is often seen in conjunction with other congenital conditions such as Down's syndrome and cleft palate, although no direct connection that would explain the correlation between diseases was found. A person with binder syndrome has a flat nasal bridge and an unusually short nose. Other noticeable disfigns are abnormally undeveloped upper jaw and protruding line of the lower jaw. Case studies of individuals with the condition have shown a family history of syndrome. Although there is evidence of family correlation, it has not been found that sound evidence shows or refutes the genetic cause. So far, no evidence has been found that shows that environmental causes are a contributing factor in the development of the syndrome.

physically, the main physical characteristic of the Binder syndrome is an extremely recessed nasal cavity that results in a flat nose. This abnormality is the wayEna absence of a structure supporting nose, referred to as nasal spine. Other physical properties of the attributed state include small incisors and missing stools.

When the patient's skull is examined under the X -ray, it is often found that two key maxillofacial structures are missing or deforming. Cartilage that divides the mouth from the nasal cavity is usually missing or seriously carried. The frontal cavities are also sometimes recorded that they are either incorrectly or smaller than the average individual.

Complications associated with binder syndrome are diverse depending on the patient. Many individuals show an increase in sinus infections. These infections are often caused by an occlusion caused by Malfemormed nasal septum that divides two nostrils. Difficulty in food is sometimes recorded because the floor is often missing or deformed. Poor intelligence was also recorded in people with Binder's syndrome, ACKOIf the exact cause has not yet been discovered.

6 During this surgery, the nose and the nasal cavity are reconstructed from the cartilage taken from the donor place on the patient or from an external donor. The missing nasal spine is rebuilt and the deviations of the septum are repaired. This not only allows the patient to have a normal appearance, but also corrects related difficulty breathing problems.

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