What is hemophilia B?

Hemophilia B is a hereditary state in which the body of a person is unable to prevent blood clotting correctly, resulting in extensive bleeding. A person with haemophilia B is susceptible to the nosebleeds and a long period of bleeding from surgery. Caused by a defective gene on X chromosome, the condition is more common in men than women. Although it is possible for a person to bleed to death from this disorder, most people are able to live a normal life with treatment, including a vaccine.

As a result of insufficiency of blood plasma protein called IX factor, one is not able to control bleeding. If the individual does not have enough protein, the blood is unable to coagulate sufficiently to handle the bleeding properly. If the protein level is not normal, there may be incidents of a long period of bleeding for any perceptible reason. Another name for haemophilia B is the Hemophilia of Factor IX.

Women are the carriers of the gene causing haemophilia B. Because women have two chromosomes x, if one chromosome x is defective, the other can compensateVat. Since men have only one X chromosome, men will have a disorder if they have one defective gene. A male child born to a woman who carries a defective chromosome X has a 50 % option to have a condition, while a female child has 50 percent possible to be a carrier. It is also possible for a person to evolve as a result of gene mutation, rather than as a result of hereditary factors.

A person suffering from haemophilia can experience serious complications. Inner bleeding can lead to pain and swelling, which can cause joint and muscle deformities. Also, the state bleeding can cause the base of the tongue to increase, causing difficulty breathing. A person with haemophilia must also be cautious, as a slight intervention in the head can result in considerable bleeding of a perch that can lead to brain damage or even death.

Typical treatment of haemophilia B involves infusion of IX factor concentrate to reduce the potential of excessive bleeding. The amount of concentrate performed depends on how serious bleeding and size arethe patient. If necessary, the infusion may be administered separately at the beginning of bleeding. A person with a serious form may require constant transfusions as well as regular visits to a hematologist. It may also be necessary for an individual with a condition to receive a vaccine against hepatitis B.

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