What is Lupus Pernio?

Health condition known as lupus pernio acute has nothing to do with lupus or gift. It is a type of sarcoidosis, the disease most known for difficulty breathing, inflammation and skin lesions. Lupus Pernio is also known as Besnier-Boeck-Schaumann's disease and is considered rare.

With this condition, the skin area becomes hard, with color from red to purple. The lesions form plaques, nodes or tumors and create a disfigured appearance. The most common areas for finding such lesions are the face, ears, nose and occasionally hands or legs. These lesions are persistent and often take weeks to respond to treatment if at all.

as chilblains or regular Pernio, Lupus Pernio could initially be missed as frostbite. Lesions caused by all these conditions can be very similar, although lupus Pernio, unlike chilblains or frostBite, is not due to the exposure to cold conditions. Instead, it is considered to be the result of immune professionary weakens, almost the sameOther scarcoidosis. In many cases, patients who show skin lesions, also treated for respiratory or pulmonary conditions such as scarcoidosis, lymphatic nodes and other lung diseases. However, these conditions are not necessarily the predecessor of Lupus Pernio.

Unlike lupus erythematosus, the condition of the most important simply known as lupus, lupus pernio is not exposed to photosensitivity. The lesions are painful if the skin breaks. Exposure of excessive sunlight can increase sensitivity and irritation, even without photosensitivity associated with traditional lupus.

lesions associated with this type of sarcoidosis can leave scars or cause permanent deformities, especially when it comes to nasal cavities and passages. In some cases, patients respond well to corticosteroids such as prednisone or other steroid drugs. However, Recurring is often required and recommended periodic treatment.

It is not known about the exact causes or properties of Lupus Pernio, beyond the belief that it is an autoimmune disease including a non -functional or abnormal immune response. Statistical data suggest that most affected patients are 20 to 40 years of age. Women are more sensitive than men. People from Puerto Rico, Irish, Scandinavian or German decents have a higher risk of developing Lupus Pernio and other forms of srckidosis.

In addition to skin lesions and respiratory problems include other symptoms of fever, fatigue, weight loss and poor appetite. Many patients report that they feel sick or feel as if they had the flu. Some patients report no symptoms outside lesions.