What are the different treatment of porphyria?
Porphyria is a term that describes eight or more types of disorders affecting the level of the hem molecule that carries oxygen around the body. The name comes from the presence of excess porphyrin molecules in the body. Various porphyria treatments include a number of blood extraction or transfusions, bone marrow transplantation, spleen removal or medicines such as hydroxychlorochin, chlorocamine, hemin, beta-carotene or activated coal. No drugs treat all porphyria. Research of genetic therapy and bone marrow or stem cell transplantation can provide effective treatment for porphyria other than medicines.
The most common porphyria is Porphyria Cutanea Tarda (PCT) with a prevalence of approximately one of every 10,000 people. About 80 percent of patients with porphyria have this type of disease. People who have PCT or other, much more rare, the type of porphyrie called hepatoerythropoetic porphyria (HEP) are in uroporphyrinogen decarboxylas insufficient enzyme. The lack of enzyme results in skin blisters and mild liver problems.
pct is the bestNoducts of all porphyria to treat. The doctor most often recommends a series of blood extraction to remove excess iron. Patients may also be treated with low doses of hydroxychlorine or chlorochin. These types of porphyria treatment are usually very successful in controlling the disease.
Congenital erythropoietic porphyria (CEP) is a very rare type of porphyria. People with CEP have a lack of enzyme uroporphyrinogen III kosyntase and their skin can show blisters and increased degree of infection along with anemia. Treatments include blood transfusions, bone marrow transplantation, activated coal as oral medicine and spleen removal.
Of all porphyria treatments, one particular medicine covers the widest range of disorders. The hemin drug is a produced form of heme, which is injected into the patient's vein. The drug regulates the concentration of raw materials of porphyrin and porphyrin in the blood. Hemin is used to treat acute intermittent porphyria (AIP),Variegate porphyria (VP), hereditary coproporphyria (HCP) and dehydratase dehydratase dehydratase delta-aminolevulin (ADP). Another remedy for these diseases is heme ariat and sometimes patients are treated with glucose.
erythropoietic protoporphyria (EPP) is a genetic disorder of the enzyme of ferrochetase. This disease is caused by photo -sensitive skin problems, problems with slaughter or bile stones. Recommended treatment for EPP is ingestion of beta-carotene.
Porphyria treatment covers the entire range of disorders. At the beginning of 2011 there was no medicine for any type of porphyrie. Doctors recommend that patients eat high carbohydrate diet, but the diet itself does not control the symptoms of the disease. Clinical studies examined the effectiveness of gene therapy, bone marrow transplantation and stem cell treatment for porphyria.