What is hereditary intolerance of fructose?
People with hereditary intolerance of fructose have a inherited condition that prevents them from digestion of sugar called fructose. Ingestion of fructose, when the body cannot digest, can cause dangerous side effects that can eventually lead to jaundice and liver disease. For this reason, people with this disorder must monitor a special hereditary diet with fructose intolerance that eliminates all sources of this sugar. Fructose is often added as a sweetener to processed food and drinks, including many baby foods. The prevalence of fructose in natural and processed foods makes this substance a complicated trade. People with fructosis intolerance have a lack of enzymes of the livernasium with Aldolas-B, which is essential for fructose metabolism. Eating fructose in the absence of this enzyme causes metabolic problems that may cause dangerously low blood sugar as well as kidney and liver toxicity. This is because Aldolyzy-B deficiency also prevents the effective use of phosphates, toTerés are needed to convert glycogen into glucose. The final result is not only hypoglycaemia, but also a dangerously high level of toxic metabolites in the liver.
Children with this disorder begin to show symptoms soon after they are first fed to patterns containing sucrose or containing fructose or other foods. In children, hereditary symptoms of fructose intolerance include poor feeding, digestive problems after food or sucrose, excessive drowsiness, irritability, vomiting, jaundice and seizures, convulsions. Possible complications include uncontrolled bleeding, liver liver, liver disease and ultimately liver failure. Some people are also at risk of DNA, as this condition can also increase the blood level of uric acid.
complete elimination of all dietary fructose is the only treatment for hereditary intolerance of fructose and there is no drug for the disorder. Diet beFrom fructose it requires the elimination of fruit and fruit products, honey of all kinds, sucrose and all foods that contain fructose or sucrose as a sweet agent. This includes syrups such as maple syrup, molasses, corn syrup and agave syrup, all of which contain fructose or sucrose. Processed foods containing one of these sweeteners should also be avoided. The prognosis for people with this disorder is good if the diet is monitored.